Darier disease: case report with oral manifestations.

نویسندگان

  • Camila Lopes Cardoso
  • Patrícia Freitas
  • Luís Antônio de Assis Taveira
  • Alberto Consolaro
چکیده

Darier disease, also known as keratosis follicularis or dyskeratosis follicularis, is a rare autosomal dominant genodermatosis. It is clinically manifested by hyperkeratotic papules primarily affecting seborrheic areas on the head, neck and thorax, with less frequent involvement of the oral mucosa. When oral manifestations are present, they primarily affect the palatal and alveolar mucosa, are usually asymptomatic, and are discovered in routine dental examination. Histologically, the lesions present suprabasal clefts in the epithelium with acantholytic and dyskeratotic cells represented by corps ronds and corps grains. This paper reports a case of an adult male patient presenting clinical signs of Darier disease in the palatal mucosa and skin on the neck and upper limbs. Intraoral biopsy of the affected area, analysis of family history and evaluation by a multidisciplinary team led to the diagnosis of Darier disease. Dental professionals and pathologists should be aware of these lesions to allow correct diagnosis and proper management of this disease.

برای دانلود رایگان متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Oral contraceptives in the treatment of Darier-White disease--a case report and review of the literature.

In this review we illustrated the case of a woman who had perimenstrual exacerbations of Darier-White disease. The disease improved markedly with the use of continuously administered oral contraceptives. This striking improvement without side-effects supports the use of oral contraceptives in women with Darier-White disease, although its role should be investigated further using controlled stud...

متن کامل

Darier disease: a case report.

The diagnosis of Darier disease of the oral mucosa was made only after biopsying a leukoplakia-like lesion of the palate.

متن کامل

Calcifying epithelial odontogenic (Pindborg) tumor involving a 16-year-old girl with no ‎prominent clinical manifestation: A case report

BACKGROUND AND AIM: The calcifying epithelial odontogenic tumor (CEOT) is a rare entity described by Pindborg and represents < 1% of all odontogenic tumors. Nearly 200 cases of this neoplasm have been reported to date. It mostly occurs in the posterior mandible associated with an impacted tooth, most often a mandibular molar. Patients are usually between 30 and 50 years of age, with no sex pred...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

عنوان ژورنال:
  • Medicina oral, patologia oral y cirugia bucal

دوره 11 5  شماره 

صفحات  -

تاریخ انتشار 2006